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南方医科大学口腔医院 口腔医学院, 广东 广州, 510015
陈亚男, E-mail: 925230876@qq.com
收稿日期:2025-04-10,
修回日期:2025-07-28,
录用日期:2025-07-29,
网络出版日期:2025-09-18,
移动端阅览
张燕, 曾小琳, 李晶, 等. 1例糖原累积病Ib型患儿全口牙病综合治疗的护理体会[DB/OL].中西医结合临床案例库, 2025.
ZHANG Yan, ZENG Xiaolin, LI Jing, et al. Comprehensive Dental Treatment and Nursing Experience for a Pediatric Patient with Glycogen Storage Disease Type Ib[DB/OL].Clinical archives of integrative medicine, 2025.
张燕, 曾小琳, 李晶, 等. 1例糖原累积病Ib型患儿全口牙病综合治疗的护理体会[DB/OL].中西医结合临床案例库, 2025. DOI: 10.12209/CAIM202504100001.
ZHANG Yan, ZENG Xiaolin, LI Jing, et al. Comprehensive Dental Treatment and Nursing Experience for a Pediatric Patient with Glycogen Storage Disease Type Ib[DB/OL].Clinical archives of integrative medicine, 2025. DOI: 10.12209/CAIM202504100001.
糖原累积病是一组由于先天性酶缺陷导致的糖原代谢障碍性疾病。本个案针对患儿低血糖、跌倒高风险因素,进行原位模拟演练、告知—演示—操作行为引导、感官脱敏训练,采用道具直观演示健康宣教方法、Teach-back教育方法及互联网+微信平台的“码”上服务的模式,提高患者及家属参与口腔健康管理的依从性,改善自我管理能力,确保干预措施的有效性和持续性。经对症治疗及护理后,患儿顺利完成患牙的充填修复或根管治疗,牙龈炎消退,8次治疗无不良事件,治疗完成率100%,2年随访口腔卫生良好,无新发龋。
Glycogen storage diseases (GSDs) are a group of inherited metabolic disorders caused by enzymatic deficiencies in glycogen metabolism. This case report focused on a pediatric patient with hypoglycemia and high risk of falls. Interventions included in-situ simulation drills, the "Tell-Show-Do" behavioral guidance technique, sensory desensitization training, visual health education using props, the Teach-back method, and an internet-based "QR code" service model via WeChat to enhance compliance with oral health management and improve self-care capabilities. These measures ensured the effectiveness and sustainability of the interventions. After targeted treatment and nursing, the child successfully completed restorative fillings or root canal therapy for affected teeth, with resolution of gingivitis. All 8 treatment sessions were completed without adverse events (completion rate: 100%). Two-year follow-up showed maintained oral hygiene with no new caries.
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DU R Y , YANG W P , LAM P P Y , et al . Developing a toothbrushing visual pedagogy (TBVP) for preschool children with autism spectrum disorder [J]. J Autism Dev Disord , 2022 , 52 ( 1 ): 327 - 338 .
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